Abstract
Systemic lupus erythematosus (SLE) is a complex disease with an etiological factor not completely understood, important morbidity and mortality, due both to autoimmune component and immunosuppressive treatment. Pseudotumor cerebri and diffuse alveolar hemorrhage are both secondary to an elevated autoimmune activity and low incidence; simultaneous is highly unlikely.
We present the case of a patient with SLE hospitalized for respiratory symptoms with a final diagnosis of a diffuse alveolar hemorrhage which favored a pseudotumor cerebri condition. Was treated with steroid pulses and plasmapheresis with adequate neurological and pulmonary response. A prompt diagnosis and treatment leads to better outcomes, especially with acute lung involvement, associated with a high mortality rate.
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