Sobreposición del síndrome de Miller Fisher y encefalitis de Bickerstaff en pediatría: reporte de caso

Autores/as

  • Víctor Manuel Rozo Hernández Neuropediatra, Hospital Universitario Fundación Santafé de Bogotá, Colombia.
  • Paul Leonardo Trigos Pallares Intensivista pediatra, Fundación Santafé.
  • Juan Nicolas Useche Gómez Neurorradiólogo, Fundación Santafé.
  • Martha Cecilia Piñeros Fernández Neuropediatra, Hospital Universitario Fundación Santafé de Bogotá, Colombia.
  • Maira Alejandra Soto Trujillo Psiquiatra infantil y de adolescentes, Fundación Santafé.

DOI:

https://doi.org/10.22379/24224022203

Palabras clave:

síndrome de Miller Fisher, Encefalitis del tallo cerebral de Bickerstaff, Anticuerpo anti-GQ1b (DeCS)

Resumen

Se describe el caso en pediatría de la sobreposición del síndrome de Miller Fisher y la encefalitis de Bickerstaff en presencia de perfil de anticuerpos positivos para anti-GQ1b en un niño de 6 años, quien presenta un compromiso tronco-encefálico y luego entra en una encefalopatía con compromiso de nervio periférico. El presente caso es relevante en relación con los escases de artículos semejantes en la literatura pediátrica, con pocos precedentes en la literatura publicada hasta la fecha.

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Odaka M, Yuki N, Yamada M, Koga M, Takemi T, Hirata K, Kuwabara S. Bickerstaff's brainstem encephalitis: clinical features of 62 cases and a subgroup associated with Guillain-Barre' syndrome. Brain. 2003;126(Pt 10):2279-90.

Cómo citar

Rozo Hernández, V. M., Trigos Pallares, P. L., Useche Gómez, J. N., Piñeros Fernández, M. C., & Soto Trujillo, M. A. (2018). Sobreposición del síndrome de Miller Fisher y encefalitis de Bickerstaff en pediatría: reporte de caso. Acta Neurológica Colombiana, 34(2), 139–145. https://doi.org/10.22379/24224022203

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Publicado

01-01-2018

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