Abstract
La Encefalitis por Anticuerpos contra el Receptor N-metil D-aspartato (NMDAR) es un trastorno grave con una presentación inicial puramente neuropsiquiátrica, que evoluciona hacia una encefalopatía severa, y es acompañado por movimientos involuntarios, convulsiones e inestabilidad autonómica; el curso de la enfermedad usualmente se prolonga y necesita tratamiento inmunomodulador agresivo. Se describe el caso de un paciente de 5 años con diagnóstico de Encefalitis por Anticuerpos contra el Receptor N-metil D-aspartato (NMDAR), manejado con tratamiento inmunomodulador, logrando así control y no progreso de enfermedad.
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