Abstract
Parry-Romberg syndrome is a neurocutaneous disorder with a not well-established etiology characterized by progressive facial hemiatrophy related to other neurological disorders such as epilepsy, migraine and trigeminal neuralgia. Clinical and radiological features of this syndrome are well known, but are still an unusual and unknown disease; therefore it is diagnosed late leading to an inadequate care and misinformation to patients.
This paper report the case of a middle aged woman with progressive facial hemiatrophy since seven years old associated with migraine and facial neuropathic pain, classical complications of this disease. Since diagnosis was made many years after de onset of symptoms, she received the proper treatment of her ophthalmologic and neurological disorders late.
References
DUYMAZ A, KARABEKMEZ FE, MUSTAFA K, ZAKERIYA T. Parry-Romberg syndrome: facial atrophy and its relationship with other regions of the body. Ann Plast Surg.. 2009; 63: 457-61.
PICHIECCHIO A, UGGETTI C, GRAZIA EGITTO M, ZAPPOLI F. Parry-Romberg syndrome with migraine and intracranial aneurysm. Neurology. 2002; 59: 606-8.
BERGLER-CZOP B, LIS-SWIETY A, BRZEZINKA-WCISTO L. Scleroderma linearis: hemiatrophia faciei progressiva (Parry-Romberg syndrom) without any changes in CNS and linear scleroderma "en coup de sabre" with CNS tumor. BMC Neurology. 2009; 9:39.
CAO QJ, WANG H. Parry-Romberg syndrome: A case report and review of literature. Journal of Chinesse Clinical Medicine. 2009; 4: 592-5.
RESTIVO DA, MILONE P. Teaching Neurolm-ages: progressive facial hemiatrophy (Parry-Romberg syndrome) with ipsilateral cerebral hemiatrophy. Neurology. 2010; 74: ell.
LAZARIDOU E, GIANNOPOULOU C, APALLA Z, FOTIADOU C, TRIGONI A, IOANNIDES D. Parry-Romberg syndrome. J Dermatol Case Rep. 2010; 2: 30-2.
PATEL H, THAKKAR C, PATEL K. Parry-Romberg syndrome: a rare entity. J Maxillofac Oral Surg. 2010; 9: 247-50.
DEFELIPE J, SEGURA T, ARELLANO JI, MER-CHÁN A, DEFELIPE-OROQUIETA J, MARTÍN P, ET.AL. Neuropathological findings in a patient with epilepsy and the Parry-Romberg syndrome. Epilepsia. 2001; 42: 1198-203.
MALETIC J, TSIRKA V, IOANNIDES P, KARA-COSTAS D, TASKOS N. Parry-Romberg Syndrome Associated with Localized Scleroderma. Case Rep Neurol. 2010; 2: 57-62.
STONE J. Parry-Romberg syndrome. Practical Neurology. 2006; 6:185-8.
STONE J. Parry-Romberg syndrome: a global survey of 205 patients using the Internet. Neurology. 2003; 61: 674-6.
PAPROCKA J, JAMROZ E, ADAMEK D, MARSZAL E, MANDERA M. Difficulties in differentiation of Parry-Romberg syndrome, unilateral facial sclerodermia, and Rasmussen síndrome. Childs Nerv Syst. 2006; 22: 409-15.
ONESTI MG, MONARCA C, RIZZO MI, MAZZOCCHI M, SCUDERI N. Minimally Invasive Combined Treatment for Parry-Romberg Syndrome. Aesth Plast Surg. 2009; 33: 452-6.
BLITSTEIN MK,VECCHIONE MJ, TUNG GA. Parry-Romberg syndrome. Applied Radiology. 2011; 40: 34-6.
This work is licensed under a Creative Commons Attribution-NonCommercial-NoDerivatives 4.0 International License.