Resumen
La enfermedad de Moyamoya es una patología cerebrovascular, de causa desconocida e infrecuente en población occidental; se reconoce como evento isquémico en la edad pediátrica, secundario a estenosis progresiva de la porción intracraneal de la arteria carótida interna y ramas principales. Esto ocasiona reducción del flujo de los vasos mayores de la circulación anterior y provoca desarrollo compensatorio de pequeños vasos colaterales; el manejo puede ser conservador o quirúrgico. Se describen 4 casos pediátricos diagnosticados, manejados y seguidos en la consulta de neuropediatria, uno de ellos corresponde a un síndrome de Moyamoya, y los otros a enfermedad, a 3 pacientes se les realizó manejo conservador y a uno amanejo quirúrgico.
Citas
FUKUI M. Guidelines for the diagnosis and treatment of spontaneous occlusion of the circle of Willis (Moyamoya disease). Research committee ion spontaneous occlusion of the circle of Willis (Moy-amoya disease) of the ministry of health and Welfare, Japan. Clin NeurolNeurosurg 1997;99:S238-40.
KURODA S, HOUDINI K. Moyamoya disease: current Concepts and future perspectives. Lancet Neurol 2008;7:1056-66.
ACHROL A, GUZMAN R, LEE M, STEINBERGG. Pathophysiology and genetics factors in Moyamoya disease. Neurosurg Focus 2009;26:E4.
JEA A, SMITH E, ROBERTSON R, SCOTT M. Moyamoya syndrome associated with Down syndrome: Outcome after surgical revascularization. Pediatrics 2005;116:694-701.
GONZÁLEZ A, CAMPISTOL A, NAVARRO B, CAPDEVILA C, SOLA T. Moyamoya en la población infantil. Análisis de una serie occidental y revisión de la bibliografía. Rev Neurol 2008;46:385-91.
GALICCHIO S, MAZA E, JAIMOVICH R, ARROYO H. Arch Arg Pediatr 1998;96:263-7.
KURIYAMA S, KUSAKA Y, FUJIMURA M,WAKAI K, TAMAKOSHI A, HASHIMOTOS, ET AL. Prevalence and clinic-epidemiological features of Moyamoya disease in Japan:findings from a nationwide epidemiological survey. Stroke 2008;39:42-7.
UCHINO K, JOHNSTON SC, BECKER KJ, TIRSCHWELL DL. Moyamoya disease in Washington State and California. Neurology 2005;65:956-8.
SMITH J. Understanding and treating Moyamoya disease in children. Neurosurgery Focus 2009;26:E4.
SMITH E, SCOTT M. Síndrome de Moyamoya. Revista Argentina de Neurocirugía 2005;19:31-40.
URRUTIA M, BARRAGÁN E, HERNÁNDEZ J, GARZA S, ET AL. Enfermedad de Moyamoya. Bol Med Hosp Infant Mex 2007;03-04:99-106.
SMITH E, SCOTT M. Síndrome de Moyamoya. Revista Argentina de Neurocirugía 2005;19:31-40.
CROSA R, WILSON D, WILSON E. Pialsinangio-sis como tratamiento en la enfermedad de Moyamoya en niños. Rev Med Urug 2007;23:192-9.
FUJIWARA H, MOMOSHIMA S, KURIBAYASHI S. Leptomeningeal high signal intensity on fluid-attenuated inversion-recovery (FLAIR) MR images in Moyamoya disease. Eur J Radiol 2005;55:224-30.
SCOTT M, SMITH E. Moyamoya disease and Moyamoya syndrome. N Eng J Med 2009;360:122637.
SUZUKI J, TAKAKU A. Cerebrovascular "Moyamoya" disease:disease showing abnormal net-like vessels in base of brain. Arch Neurol 1969;20:288-99.
BOWEN M, BURAK C, ET AL. Childhood ischemic stroke in a nonurban population. J Child Neurol 2005;20:194-7.
NOMURA S, KASHIWAGI S, UETSUKA S, UCHIDA T, KUBOTA H, ITO H. Perioperative management protocols for children with Moyamoya disease. Child Nerv Syst 2001;17:270-4.
ROACH S, MEREDITH R. ET AL. Management of Stroke in Infants and Children. A Scientific Statement for Healthcare Professionals from a Special Writing Group of the Stroke Council, American Heart Association. Stroke 2008;39:2644-91.
CALDERELLI M, DI ROCCO C, GAGLINI P. Surgical treatment of Moyamoya disease in pediatric age. J Neurosurg Sci 2001;24:85-91.
VEERAVAGU A, GUZMAN R, PATH CG, HOU LC, LEE M, STEINBERG GK. Moyamoya disease in pediatric patients:outcomes of neurosurgical interventions. Neurosurg Focus 2008;24(E16):1-9.
BACIGALUPPI S, DEHDASHTI A. ET AL. The contribution of imaging in diagnosis, preoperative assessment, and follow-up of Moyamoya disease. A review Neurosurg Focus 2009;26:E3.
REIS C, SAFAVI-ABBASI S, ZABRAMSKI J, ET AL. The history of neurosurgical procedures for Moyamoya disease. Neurosurg Focus 2006;20:E7.
IKEZAKI K. Rational approach to treatment of Moyamoya disease in childhood. J Child Neurol 2000;15:350-6.
BAAJ A, AGAZZI S, SAYED Z, TOLEDO M, ET AL. Surgical management of Moyamoya disease:A review. Neurosurg Focus 2009;26:E7.
Esta obra está bajo una licencia internacional Creative Commons Atribución-NoComercial-SinDerivadas 4.0.